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disease > skin appendages disease > skin disease > pigmentation disorder > phakomatosis pigmentovascularis
disease > congenital disease > phacomatosis > phakomatosis pigmentovascularis

Término preferido

phakomatosis pigmentovascularis  

Definición

  • Phakomatosis pigmentovascularis is a rare neurocutanous condition where there is coexistence of a capillary malformation (port-wine stain) with various melanocytic lesions, including dermal melanocytosis (Mongolian spots), nevus spilus, and nevus of Ota. (Wikipedia)

etiqueta alternativa (skos)

  • phacomatosis pigmentovascularis

En otras lenguas

URI

http://data.loterre.fr/ark:/67375/VH8-LV15KLGQ-N

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