Concept information
Preferred term
bullous ichtyosiform erythroderma
Definition(s)
- Epidermolytic ichthyosis (EI), also known as bullous epidermis ichthyosis (BEI), epidermolytic hyperkeratosis (EHK), bullous congenital ichthyosiform erythroderma (BCIE), bullous ichthyosiform erythroderma or bullous congenital ichthyosiform erythroderma Brocq, is a rare and severe form of ichthyosis this skin disease affects around 1 in 300,000 people. (Wikipedia)
Broader concept(s)
Synonym(s)
- epidermolytic hyperkeratosis
In other languages
-
French
-
hyperkératose épidermolytique
URI
http://data.loterre.fr/ark:/67375/VH8-C4NHTKSL-L
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